Pseudoxanthoma elasticum in a patient with sickle cell disease: case report
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Date
2008Author
Adam, A. M.
Maritim, Marybeth C
Type
ArticleLanguage
enMetadata
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An 18 year female sickler (HbSS) presented with repeated history of epistaxis and bleeding gums. Features consistent with pseudoxanthoma elasticum were observed, such as hyper-extensile redundant skin folds in the neck, axilla, inguinal areas and abdomen. The skin biopsy showed swollen, clumped and fragmented elastic fibres and calcium deposits in the deep and mid reticular dermis, consistent with pseudoxanthoma elasticum. This is a well recognised complication of sickle cell disease which has not been described in Kenya
URI
http://erepository.uonbi.ac.ke:8080/xmlui/handle/123456789/16328http://www.ncbi.nlm.nih.gov/pubmed/18557254
Citation
East Afr Med JPublisher
Department of Medicine. College of Health Sciences. University of Nairobi
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- Faculty of Health Sciences (FHS) [10377]