Congenital cystic adenomatoid malformation of lung type 1.
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Date
2010Author
Mathai, AM
Kini, H
Pai, MR
Shetty, AB
Murali, N
Type
ArticleLanguage
enMetadata
Show full item recordAbstract
Congenital cystic adenomatoid malformation, a rare developmental, hamartomatous abnormality of the lung, usually is unilateral, is localized, and presents in early infancy. Delayed occurrence in older children and multilobar involvement are rare. We describe a case of congenital cystic adenomatoid malformation type 1 with multilobar involvement, associated emphysema, and coexistent tracheobronchopathia osteochondroplastica in an adolescent girl for whom the correct diagnosis was achieved only on histologic examination. The importance of an accurate diagnosis of this entity enables proper subtyping, management to minimize the risk of infections and malignancy, and exclusion of associated malformations.
URI
http://erepository.uonbi.ac.ke:8080/xmlui/handle/123456789/58113http://www.ncbi.nlm.nih.gov/pubmed/20152335
Publisher
University of Nairobi College of Health Science
Collections
- Faculty of Health Sciences (FHS) [10387]